Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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Enfermedad de Hirschsprung

Mechanisms of idiopathic constipation: An analysis of patients. Medicina de Caldas, vol. Rectal suction biopsy in the diagnosis of Hirschsprung’s disease: Hirschsprung disease and hypoganglionosis in adults: Reliability of intraoperative frozen sections in the management of Hirschsprung’s disease.

Bowel function, mental health, and psychosocial function in adolescents with Hirschsprung’s disease. Between July and June27 children were identified with HD.

All patients with HD enfermwdad had definitive surgery at the Queen Elizabeth Hospital, Barbados, over a year period between July and June were identified from the hospital records system. However, many factors outlined by Somme 8 which will affect earlier diagnosis and referral have improved and will continue to improve throughout the Caribbean. Kirschsprung Like sindromes in patients with normal ganglion cells on suction rectal biopsy. Two children had cousins with HD enfermedqd one child had an older sibling with the condition.

These include the limited number of paediatric surgical specialists and support staff and lack of facilities and equipment for the handling of frozen section specimens as well as paediatric pathologists trained to read and interpret frozen section specimens. Six of the children presenting in the neonatal period, did so within 48 hours of life with intestinal obstruction vomiting and abdominal distension and had laparotomy. During the review of patients’ records in this study, it was clear that a number of children who initially presented in the neonatal period and re-presented later in childhood were being treated for necrotizing enterocolitis NEC in the neonatal period when most likely they were experiencing Hirschsprung’s enterocolitis.


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Primary laparoscopic pullthrough for Hirschsprung’s disease in infants and children. Progress in management and diagnostics. Primary versus staged pull-through for the treatment of Hirschsprung disease. Article in pdf format Article in xml format Article references How to cite this article Automatic translation Send this article by e-mail.

Diagnostic Imaging in children with acute chest and abdominal disorders. False-positive intra-operative frozen sections reported in centres where experienced pathologists are unavailable can have serious consequences Transanal endorectal pull-through for Hirschsprung’s disease. The adults consult for a chronic constipation history, abdominal distension, use of laxatives and enemas since childhood.

Enfermedad de Hirschsprung | Women on Wellness

hifschsprung The diagnostic is supported with studies of the barium enema, anorectal manometry and inmunohistochemestry. Idiopathic Disorders of fecal continence in children. However you have to be at the expectation of the results when the patient defecates after the enfermddad, because it can present fecal incontinence or constipation.

Comparison with c1inical amI radiological criteria. The 11 children excluded from long-term follow-up included two with total colonic HD – one of whom had definitive surgery elsewhere, three who were lost to follow-up, one child whose parents declined to take part in the study, one child awaiting definitive surgery, one child who had a stoma at the time of study and three who did not have a Martin’s modified Duhamel procedure as definitive surgery for HD.

The affected bowel is of smaller caliber and thus depending on the length of segment affected variable amounts of colonic distension are present. Articles Cases Courses Quiz.


There were no associated chromosomal anomalies, however one child had congenital auricular atresia. Findings are primarily those of a bowel obstruction. None of the questionnaires were completed by the operating surgeon SUJ.

Diagnosis of congenital megacolon: Megaeystis Illicrocolonintestinal hypoperistalsis synorollle: Three of the children had a positive family history of HD.

Enfermedad de Hirschsprung | Medicina

Where this is successful, the prognosis is good. In protracted cases, marked dilatation can develop, which may progress to enterocolitis and perforation. While transportation and poor communication systems may indeed be a challenge for the Caribbean, especially in the presence of multiple small islands, a number of factors make routine use of the enfermeedad pull-through procedure inappropriate for the Caribbean, if not impossible.

Enterocolitis complicating Hirschsprung’s disease.

It should be noted however that the depicted transition zone on the contrast enema is not accurate at determining the transition between absent and present ganglion cells.

Hirschsprung disease in the newborn. Endorectal pull-through without preliminary colostomy on neonates with Hirschsprung’s disease. Primary aganglionosis associated with imperforate anus review of the litcraturc pcrtinent to one observation.

A new surgical approach to extensive aganglionosis. Organic constipalion in adults.

Synonyms or Alternate Spellings: The majority of patients with Hirschsprung’s disease HD have a satisfactory outcome after definitive surgery 3. Ineluding sixty-seven consecutive Endorectal Pullthrough procedures. It is hisrchsprung known fact that the clinical features of NEC – foul-smelling, explosive diarrhoea, often bloody in nature, abdominal distention, hypovolaemic shock, vomiting, fever and lethargy may mimic that of Hirschsprung’s enterocolitis.